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jsmc-10086


EPIDEMIOLOGY OF ESOPHAGEAL ATRESIA: A HOSPITAL-BASED STUDY IN SULAIMANI


Nian N. Ameen *


* Department of Surgery, School of Medicine, Faculty of Medical Sciences, University of Sulaimani.


Submitted: 2/7/2015; Accepted: 22/12/2015Published: 1/6/2016


ABSTRACT


Background 

Esophageal Atresia (AE) is a sporadic unpreventable birth defect, consisting of lack of continuity between the upper and lower esophageal pouches, with prevalence rate 1-5/10 000.

Objective

The aim of this study is to describe some epidemiologic data on esophageal atresia, estimating it’s prevalence in Sulaimani province, and characterizing the cases with regards to age at presentation, gender, gestational age, pathological classification, associated anomalies, postoperative complication, and mortality rate.

Methods

This study extended from June 2006 to December 2014, in which 100 patients with esophageal atresia were managed in Pediatric Surgical Unit of Sulaimani Teaching Hospital in Sulaimani province.

Results

The total number of cases was 100 patients (61 males and 39 females), the mean gestational age was (37) weeks, and 56% had birth weight > 2500 gm. The most common type was [EA] with [TEF] (92%), thirty two percent presented between 3-7 days of age. Sixty percent of the patients developed postoperative complications; the
overall birth prevalence rate in Sulaimani was 4.7 cases per10 000 live birth. The mortality rate was (69%).

Conclusion

Esophageal Atresia is a rare disease in Sulaimani, with the most common type being Esophageal Atresia with distal tracheoesophageal fistula. Unlike other studies, in the age of presentation, those presented after the first week, had higher survival rate.

KEYWORDS

Esophageal Atresia, Tracheoesophageal fistula, Epidemiology, Sulaimani.

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